Search on: HEMOPHILIA A 
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Descriptor English:   Hemophilia A 
Descriptor Spanish:   Hemofilia A 
Descriptor Portuguese:   Hemofilia A 
Synonyms English:   Autosomal Hemophilia A
Classic Hemophilia
Deficiency, Factor VIII
Factor 8 Deficiency, Congenital
Factor VIII Deficiency, Congenital
Haemophilia
Hemophilia A, Congenital
Hemophilia, Classic
As, Autosomal Hemophilia
Autosomal Hemophilia As
Classic Hemophilias
Congenital Hemophilia A
Congenital Hemophilia As
Hemophilia A, Autosomal
Hemophilia As
Hemophilia As, Autosomal
Hemophilia As, Congenital
Hemophilias, Classic
Factor VIII Deficiency
Hemophilia  
Tree Number:   C15.378.100.100.500
C15.378.100.141.500
C15.378.463.500
C16.320.099.500
Definition English:   The classic hemophilia resulting from a deficiency of factor VIII. It is an inherited disorder of blood coagulation characterized by a permanent tendency to hemorrhage. 
See Related English:   Factor VIII
Hemarthrosis
Hemophilia B
 
History Note English:   99(66) 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications DI diagnosis
DG diagnostic imaging DH diet therapy
DT drug therapy EC economics
EM embryology EN enzymology
EP epidemiology EH ethnology
ET etiology GE genetics
HI history IM immunology
ME metabolism MI microbiology
MO mortality NU nursing
PS parasitology PA pathology
PP physiopathology PC prevention & control
PX psychology RT radiotherapy
RH rehabilitation SU surgery
TH therapy UR urine
VE veterinary VI virology
Record Number:   6619 
Unique Identifier:   D006467 

Occurrence in VHL:
 

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